Abstract：Objective: To summarize the diagnostic and treatment experiences for rare adrenal area tumors. Methods: Between January 2010 and December 2016, a total of 21 patients (10 men and 11 women with an age ranging from 8-73 years, mean 45 years) with adrenal area tumors were treated in our urological department. The data of those patients were analyzed retrospectively. All the patients received surgical operation and obtained pathological results. There were 4 cases of rare adrenal metastatic tumors, 3 cases of cortical adenocacinoma, 3 cases of myelolipoma, 3 cases of ganglioneuroma, 2 cases of malignant pheochromocytoma, 2 cases of neuroblastoma, 1 case of oncocytoma, 1 case of lymphoma and 2 cases of rare primary retroperitoneal tumors. The right diagnoses were acquired only in 6 cases before operation. Radical resection was carried out in 18 cases and partial resection in 3 cases, and vicinal organs were cut together in 3 cases. Results: All the patients received surgical operation and obtained pathological results. Ther were 4 cases of rare adrenal metastatic tumors, 3 cases of cortical adenocacinoma, 3 cases of myelolipoma, 3 cases of ganglioneuroma, 2 cases of malignant pheochromocytoma, 2 cases of neuroblastoma, 1 case of oncocytoma, 1 case of lymphoma and 2 cases of rare primary retroperitoneal tumors. The right diagnoses were acquired only in 6 cases before operation. Radical resection was carried out in 18 cases and partial resection in 3 cases, and vicinal organs were cut together in 3 cases. Conclusions: Preoperative diagnosis was very difficult for the rare adrenal area tumors and surgical therapy remained the first choice of treatment.
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